Showing all 12 results

  • Mitochondrial myopathy with hyperlactosis and stroke-like episodes (MELAS syndrome)

    L-arginine

    【Product name】Argi-U

    [English common name]L-Arginine

    [Chinese common name]L-arginine

    [English name](S)-2-Amino-5-guanidinopentanoic acid, L-protein amino acid

    [Chinese other name]2-amino-5-mercaptovaleric acid, L-protein amino acid

    [Indications] For the adjuvant treatment of diseases such as hepatic encephalopathy.

    [Usage and dosage] Oral. 3 to 6 tablets at a time, 3 times a day.

    [Storage] Sealed and stored in a dry place.

    [Tips] Some of the information on this site comes from the Internet and is only used internally by pharmacists or medical staff. It is not a substitute for doctors to diagnose face to face. Please consult a professional pharmacist for specific medications. Please refer to the actual product manual or the actual product for the product content.

  • Mitochondrial myopathy with hyperlactosis and stroke-like episodes (MELAS syndrome)

    Adenosine triphosphate (ATP)

    【Product name】Adenosine

    [English common name]Adenosine triphophate

    [Chinese common name] adenosine triphosphate (ATP)

    [English name]

    [Chinese other name]

    [Indications] for heart failure, myocarditis, myocardial infarction, cerebral arteriosclerosis, coronary arteriosclerosis, angina pectoris, paroxysmal tachycardia, acute poliomyelitis, progressive amyotrophic disease, hepatitis, nephritis, visual fatigue, Ophthalmoplegia, retinal hemorrhage, central retinitis, optic neuritis, optic atrophy, etc. This product is not easy to penetrate the cell membrane, can play its physiological effects, it is doubtful. Its energy injection is a compound injection formulated with this product and coenzyme A for hepatitis, nephritis, heart failure and the like. It has been reported that this product can inhibit the slow calcium influx of slow-reacting fibers in animal experiments, block or delay the forward and reverse conduction of the bypass; in addition, it has a transient effect of enhancing the vagus nerve, thus terminating atrioventricular nodal reentry and Arrhythmia caused by bypass reentry mechanism. It is now used to treat rapid supraventricular arrhythmias. It has the advantages of fast cardioversion and re-use in a short period of time, so it can be used to terminate supraventricular acute attacks.

    [Usage and dosage] intravenous injection. Dilute with 25% glucose injection and slowly inject. Intravenous drip. After instillation with 500 ml of 5% glucose injection, the instillation was carried out. Intramuscular injection. After injecting 2 ml of sodium chloride injection, it was injected. One day, 2-6 weeks for a course of treatment.

    [Storage] sealed, kept in a cool place (not more than 20 ° C).

    [Tips] Some of the information on this site comes from the Internet and is only used internally by pharmacists or medical staff. It is not a substitute for doctors to diagnose face to face. Please consult a professional pharmacist for specific medications. Please refer to the actual product manual or the actual product for the product content.

  • Mitochondrial myopathy with hyperlactosis and stroke-like episodes (MELAS syndrome)

    Sodium dichloroacetate

    【Product name】Sodium Dichloroacetate

    [English common name]Sodium dichloroacetate

    [Chinese common name]Sodium dichloroacetate

    [English name]Acetic acid, 2,2-dichloro-, sodium salt

    [Chinese other name]Sodium 2,2-dichloroacetate

    [indications]

    【Dosage】

    [Storage]

    [Tips] Some of the information on this site comes from the Internet and is only used internally by pharmacists or medical staff. It is not a substitute for doctors to diagnose face to face. Please consult a professional pharmacist for specific medications. Please refer to the actual product manual or the actual product for the product content.

  • Mitochondrial myopathy with hyperlactosis and stroke-like episodes (MELAS syndrome)

    Edaravone

    【Product name】EDARAVONE, RADICAVA, RADICUT

    [English common name]Edaravone

    [Chinese common name]Edaravone

    [English name]Edaravone Injection, 3-methyl -1- phenyl -2- pyrazoline -5- ketone

    [Chinese other name]Edaravone injection, 3-methyl-1-phenyl-2-pyrazol-5-one

    [indications]
    Edaravone: This product can scavenge free radicals, inhibit lipid peroxidation, thereby inhibiting oxidative disorders of brain cells (vascular endothelial cells, nerve cells), inhibiting blood flow in peripheral areas of infarction, and acting on acute phase of cerebral infarction. It inhibits the occurrence and progression (deterioration) of ischemic cerebrovascular disorders such as cerebral edema, cerebral infarction, neurological symptoms, and delayed neuronal death.
    Edaravone Injection: This product is used to improve neurological symptoms, activities of daily living and dysfunction caused by acute cerebral infarction.

    【Dosage】
    Edaravone: usually adult edaravone 30mg, 2 times / d, when diluted with appropriate amount of normal saline, intravenous infusion within 30min. The administration started within 24 hours after the onset of the disease, and the course of treatment was 14 days.
    Edaravone injection:
    1. Once 30mg (1), add intravenous saline before dilution, and then drip in 30 minutes. 2 times a day, 14 days for a course of treatment.
    2. Start dosing as soon as possible within 24 hours after onset.

    [Storage]
    Indara: Sealed and placed in a cool place.
    Edaravone injection: sealed, placed in a cool place.

    [Tips] Some of the information on this site comes from the Internet and is only used internally by pharmacists or medical staff. It is not a substitute for doctors to diagnose face to face. Please consult a professional pharmacist for specific medications. Please refer to the actual product manual or the actual product for the product content.

  • Glutaric acidemia , Mitochondrial myopathy

    Riboflavin

    【Product name】RADICUT

    [English common name]Riboflavin

    [Chinese common name]Riboflavin

    [English name]B vitamin two, Vitamin B2

    [Chinese other name]B vitamin II, vitamin B2

    [indications]
    Sodium riboflavin sodium for injection: riboflavin supplement. For the treatment of diseases such as keratitis, cheilitis, glossitis, conjunctivitis and scrotal inflammation caused by riboflavin deficiency.
    Riboflavin tetrabutyrate capsule: for the treatment of thrombosis, atherosclerosis. Can also be used for vitamin B2 deficiency, oral ulcers, scrotal inflammation, seborrheic dermatitis.
    Riboflavin sodium injection: for the treatment of keratitis, cheilitis, glossitis, conjunctivitis and scrotal inflammation.
    Riboflavin tetrabutyrate tablets: for the treatment of thrombosis, atherosclerosis. Can also be used for vitamin B2 deficiency, oral ulcers, scrotal inflammation, seborrheic dermatitis.
    Riboflavin tetrabutyrate: for the treatment of thrombosis, atherosclerosis. Can also be used for vitamin B2 deficiency, oral ulcers, scrotal inflammation, seborrheic dermatitis.

    【Dosage】
    Sodium riboflavin for injection: subcutaneous, intramuscular or intravenous. 5 to 30 mg once a day, once a day.
    Riboflavin tetrabutyrate capsules: subcutaneous, intramuscular or intravenous. 5-30mg (0.5-3) at a time, once a day.
    Riboflavin sodium injection: Oral.
    1. Thromboembolic disease: 0.1 to 0.2 g once, 3 times a day.
    2. Vitamin B2 deficiency: 0.2g once, once a day.
    Riboflavin tetrabutyrate tablets: oral.
    1. Thromboembolic disease: 0.1 to 0.2 g (1-2 tablets) at a time, 3 times a day.
    2. Vitamin B2 deficiency: 0.2g (2 tablets) at a time, once a day.
    Riboflavin tetrabutyrate: Oral, as prescribed.

    [Storage]
    Sodium riboflavin sodium for injection: protected from light and sealed.
    Riboflavin tetrabutyrate capsule: sealed and preserved.
    Riboflavin sodium injection: protected from light and sealed.
    Riboflavin tetrabutyrate tablets: shading, sealed and preserved.
    Riboflavin tetrabutyrate: shading, sealed and preserved.

    [Tips] Some of the information on this site comes from the Internet and is only used internally by pharmacists or medical staff. It is not a substitute for doctors to diagnose face to face. Please consult a professional pharmacist for specific medications. Please refer to the actual product manual or the actual product for the product content.

  • Mitochondrial myopathy , Mitochondrial myopathy with hyperlactosis and stroke-like episodes (MELAS syndrome)

    Nicotinamide

    【Product name】Brillian-VB3

    [English common name]Nicotinamide

    [Chinese common name]Nicotinamide

    [English name]Niacin, Vitamin B3

    [Chinese other name]Nicotinamide, vitamin B3

    [indications]
    Nicotinamide tablets: used to prevent and treat niacin deficiency, such as pellagra.
    Nicotinamide for injection: This product is mainly used for the prevention and treatment of niacin deficiency pellagra,Coronary heart disease, viral myocarditis, rheumatic myocarditis and a small number of digital arrhythmias associated with digitalis poisoning, have the role of prevention and treatment of heart block.

    【Dosage】
    Nicotinamide tablets: 0.1 g usage is as follows: oral. Adults, 0.5-2 tablets at a time, 5 tablets a day. The 50 mg usage is as follows: oral, adult, 1-4 tablets at a time, 10 tablets a day.
    Nicotinamide for injection: once 300 ~ 400mg, once a day. An intravenous drop of 250 ml of a 10% glucose solution was added. 30 days is a course of treatment.

    [Storage]
    Nicotinamide tablets: shading, sealed and preserved.
    Nicotinamide for injection: shading, sealed storage.

    [Tips] Some of the information on this site comes from the Internet and is only used internally by pharmacists or medical staff. It is not a substitute for doctors to diagnose face to face. Please consult a professional pharmacist for specific medications. Please refer to the actual product manual or the actual product for the product content.

  • Mitochondrial myopathy , Mitochondrial myopathy with hyperlactosis and stroke-like episodes (MELAS syndrome)

    Thiamine

    【Product name】METABOLIN

    [English common name]Thiamine

    [Chinese common name]Thiamine

    [English name]Vitamin B1, Anti – beriberi factor

    [Chinese other name]Vitamin B1, anti-foot disease factor

    [Indications] Electrolytes, vitamin B1 and amino acids in water supply
    • Insufficient oral intake if it is in mild hypoproteinemia or mildly low nutritional status.

    【Dosage】The recommended daily intake for adults is 1.0 to 1.5 mg.PregnancyIngestion, 1.5 to 1.6 mg per day during lactation;

    [Storage]It is mainly divided into storage methods or conditions such as normal temperature, cold place, cool place, cool and dark place.

    [Tips] Some of the information on this site comes from the Internet and is only used internally by pharmacists or medical staff. It is not a substitute for doctors to diagnose face to face. Please consult a professional pharmacist for specific medications. Please refer to the actual product manual or the actual product for the product content.

  • Porphyrin , Citrullineemia

    Arginine

    【Product name】Spedifen

    [English common name]L-Arginine

    [Chinese common name]Arginine

    [English name]

    [Chinese other name]

    [indications]
    Arginine hydrochloride tablets: for the adjuvant treatment of diseases such as hepatic encephalopathy.
    Arginine hydrochloride injection: for hepatic encephalopathy, suitable for patients with sodium, but also for the treatment of mental symptoms caused by other causes of blood ammonia.
    Arginine hydrochloride for injection: for hepatic encephalopathy, suitable for patients with sodium, but also for the treatment of psychiatric symptoms caused by other causes of blood ammonia.
    Arginine aspirin tablets: used for fever caused by the common cold or influenza, but also used to relieve mild to moderate pain such as headache, joint pain, migraine, toothache, muscle pain, neuralgia, dysmenorrhea.
    Arginine ibuprofen granules: for the following symptoms: toothache, dysmenorrhea, pain caused by trauma (eg sports injuries), joint and ligament pain, back pain, headache, neuralgia, and fever caused by the flu.
    Arginine ibuprofen tablets: for the following symptoms: toothache, dysmenorrhea, pain caused by trauma (eg sports injuries), joint and ligament pain, back pain, headache, and fever caused by the flu.
    Arginine hydrochloride glucose injection: for all kinds of patients with hepatic coma.

    【Dosage】
    Arginine hydrochloride tablets: oral. 3 to 6 tablets at a time, 3 times a day.
    Arginine hydrochloride injection: before use, diluted with 5% glucose injection 1000ml and applied. Intravenous infusion once 15-20g was completed within 4 hours.
    Arginine hydrochloride for injection: Before use, it is dissolved and diluted with 5% glucose injection 1000 ml and applied. Intravenous infusion once 15 ~ 20g within 4 hours drip or as directed.
    Arginine Aspirin Tablets: Oral: 0.5g once a day (based on acetylsalicylic acid), 2 to 3 times a day, or as directed by a physician.
    Arginine ibuprofen granules:
    1. Adults and patients over 12 years of age, usually oral dose: 0.4g (1 pack), 2-3 times a day.
    2. Put the medicine into the water cup, add the appropriate amount of warm water, and mix it until the liquid is completely dissolved. Taking this product on an empty stomach works more quickly. Generally do not exceed 1.2g (3 packs) per day, or use under the guidance of a doctor.
    Arginine ibuprofen tablets: 0.2 g (based on ibuprofen) usage is as follows: oral. Adults and patients over 12 years old, 0.2 g (1 tablet) at a time, 3 to 4 times a day. The usage of 0.4 g (in terms of ibuprofen) is as follows: oral, adult and patients over 12 years old, 0.4 g (1 tablet) at a time, 2 times a day.
    Arginine hydrochloride glucose injection: intravenous drip. 15 ~ 20g once, drip more than 4 hours or as directed by your doctor.

    [Storage]
    Arginine hydrochloride tablets: sealed and stored in a dry place.
    Arginine hydrochloride injection: sealed storage.
    Arginine hydrochloride for injection: sealed and stored.
    Arginine aspirin tablets: placed in a cool dry place.
    Arginine ibuprofen granules: shading, sealed, in a cool dry place.
    Arginine ibuprofen tablets: stored in a cool dry place.
    Arginine hydrochloride glucose injection: sealed storage.

    [Tips] Some of the information on this site comes from the Internet and is only used internally by pharmacists or medical staff. It is not a substitute for doctors to diagnose face to face. Please consult a professional pharmacist for specific medications. Please refer to the actual product manual or the actual product for the product content.

  • Mitochondrial myopathy with hyperlactosis and stroke-like episodes (MELAS syndrome)

    Vitamin B6

    【Product name】Vitamin B6 Injektion 

    [English common name]Vit B6

    [Chinese common name]Vitamin B6

    [English name]PYRIDOXIN

    [Chinese other name]Pyridoxine

    [indications]
    Vitamin B6 Ointment: For acne, rosacea, seborrheic eczema, wrinkle disease.
    Vitamin B6 injection: This product is suitable for:
    1. It is suitable for the prevention and treatment of vitamin B6 deficiency, prevention and treatment of isoniazid poisoning; it can also be used for vomiting caused by pregnancy, radiation sickness and anticancer drugs, seborrheic dermatitis and so on.
    2. Total parenteral nutrition and vitamin B6 supplementation due to malnutrition due to inadequate intake and progressive weight loss.
    3. The following conditions increase the amount of vitamin B6 required, pregnancy and lactation,thyroidHyperfunction, burns, chronic infection, fever, congenital metabolic disorders (cystatin, hyperoxalate, homocystinuria, uric aciduria), congestive heart failure, long-term blood Dialysis, malabsorption syndrome with hepatobiliary diseases (such as alcoholism with cirrhosis), intestinal diseases (Celiac disease, tropical inflammatory bowel disease, localized enteritis, persistent diarrhea)
    Melatonin Vitamin B6 Capsule: Improves sleep.
    Vitamin B6 for injection:
    1. It is suitable for the prevention and treatment of vitamin B6 deficiency, prevention and treatment of isoniazid poisoning; it can also be used for vomiting caused by pregnancy, radiation sickness and anticancer drugs, seborrheic dermatitis and so on.
    2. Total parenteral nutrition and vitamin B6 supplementation due to malnutrition due to inadequate intake and progressive weight loss.
    3. The following conditions increase the demand for vitamin B6: pregnancy and lactation, hyperthyroidism, burns, chronic infection, fever, congenital metabolic disorder (cystatin, hyperoxalate, homocysteine Urinary dysfunction, urtic aciduria), congestive heart failure, long-term hemodialysis, malabsorption syndrome with hepatobiliary diseases (such as alcoholism with cirrhosis), intestinal diseases (Celiac disease, tropical inflammatory bowel disease, limitations Enteritis, persistent diarrhea), after gastrectomy.
    Vitamin B6 tablets: It is suitable for the prevention and treatment of vitamin B6 deficiency, prevention and treatment of isoniazid poisoning; it can also be used for vomiting and seborrheic dermatitis caused by radiation sickness and anticancer drugs.
    Sodium Cantharidate Vitamin B6 Injection: Antineoplastic Agent. Ai Yi is comfortable for the treatment of advanced primary liver cancer and advanced lung cancer.

    【Dosage】
    Vitamin B6 Ointment: This product is for external use. Apply the ointment to the affected area 2-3 times a day.
    Vitamin B6 injection: subcutaneous injection, intramuscular or intravenous injection:
    1.1 times 50mg ~ 100mg, once a day.
    2. Detoxification of cycloserine poisoning, 300mg or more per day.
    3. When isoniazid poisoning and detoxification, 1g of vitamin B6 is given intravenously per 1g of isoniazid.
    Melatonin Vitamin B6 Capsules: 1 capsule once a day.
    Vitamin B6 for injection:
    1. Dissolve with water for injection before use, subcutaneous injection, intramuscular or intravenous injection, once 50mg ~ 100mg, once a day.
    2. For detoxification of cycloserine poisoning, 300mg or more per day.
    3. For isoniazid poisoning and detoxification, 1g of vitamin B6 is given intravenously per 1g of isoniazid. Or follow the doctor's advice.
    Vitamin B6 tablets: oral administration, adult
    1. Vitamin B6-dependent syndrome, starting from 30 to 600 mg a day, maintaining a daily dose of 50 mg, for life.
    2. Vitamin B6 deficiency, 10 to 20 mg a day for 3 weeks, 2 to 3 mg for the next day, for several weeks.
    3. Congenital metabolic disorders (cystatin, high oxalic aciduria, homocystinuria, uric aciduria), 100-500 mg daily.
    4. The drug causes a deficiency in vitamin B6.
    (1) Prevention, 10 to 50 mg per day (when penicillamine is used), or 100 to 300 mg per day (when cycloserine, ethionamide or isoniazid is used).
    (2) Treatment, 50 to 200 mg a day for 3 weeks, then 25 to 100 mg per day.
    Sodium Cantharidate Vitamin B6 Injection: Intravenous infusion, once a day. Each time 10 to 50 ml, diluted with 0.9% sodium chloride or 5% to 10% glucose injection, and then instilled.

    [Storage]
    Vitamin B6 ointment: sealed and stored in shade.
    Vitamin B6 injection: shading, sealed and preserved.
    Melatonin Vitamin B6 Capsule: Protect from light, cool and dry place.
    Vitamin B6 for injection: sealed.
    Vitamin B6 tablets: shading, sealed and preserved.
    Sodium cantharidate vitamin B6 injection: shading, confined preservation.

    [Tips] Some of the information on this site comes from the Internet and is only used internally by pharmacists or medical staff. It is not a substitute for doctors to diagnose face to face. Please consult a professional pharmacist for specific medications. Please refer to the actual product manual or the actual product for the product content.

  • Beta-ketothiolase deficiency , Propionic acidemia

    Carnitine

    【Product name】L-Carn, NICETILE, Burgerstein

    [English common name]Carnitine

    [Chinese common name]Carnitine

    [English name]DL-Carnitine

    [Chinese other name]DL-carnitine

    [indications]
    L-carnitine weight loss capsule: slimming.
    L-carnitine tablets: promote fat burning, help to quickly break down the waist, abdomen, arms, accumulated fat, reshape the fascinating curve.

    【Dosage】
    L-carnitine slimming capsules: 2 times a day, 2 capsules each time.
    L-carnitine tablets: 2 tablets each time, 2 times a day, chewing or swallowing, drink plenty of water. It is recommended to use half an hour before exercise and half an hour before meal.

    [Storage]
    L-carnitine slimming capsule: sealed, placed in a cool dry place.
    L-carnitine tablets: sealed, placed in a cool dry place.

    [Tips] Some of the information on this site comes from the Internet and is only used internally by pharmacists or medical staff. It is not a substitute for doctors to diagnose face to face. Please consult a professional pharmacist for specific medications. Please refer to the actual product manual or the actual product for the product content.

  • Medium chain acyl-CoA dehydrogenase deficiency , Mitochondrial myopathy with hyperlactosis and stroke-like episodes (MELAS syndrome)

    Coenzyme A

    【Product name】COEMZYMEA

    [English common name]Coenzyme A

    [Chinese common name]Coenzyme A

    [English name]

    [Chinese other name]

    [Indications] This product is used for acute and chronic hepatitis, primary thrombocytopenic purpura, leukocyte and thrombocytopenia caused by radiotherapy; less caused by coronary arteriosclerosis, chronic arteritis, myocardial infarction, renal insufficiency Urine, uremia, etc. have certain adjuvant treatment effects.

    [Usage and Dosage] This product is injected intramuscularly, 50-200 units per unit, 50~400 units per day, and dissolved in 2ml of sodium chloride injection before use.

    [Storage] Sealed and stored in a cool dark place (not to exceed 20 °C).

    [Tips] Some of the information on this site comes from the Internet and is only used internally by pharmacists or medical staff. It is not a substitute for doctors to diagnose face to face. Please consult a professional pharmacist for specific medications. Please refer to the actual product manual or the actual product for the product content.

  • Leber hereditary optic neuropathy , Mitochondrial myopathy

    Coenzyme Q10

    【Product name】Coenzyme

    [English common name]Coenzyme Q10

    [Chinese common name]Coenzyme Q10

    [English name]Natural quinone, Ubiquinone 10

    [Chinese other name]Terpene, ubiquinone 10

    [Indications] This product is used for adjuvant treatment of the following diseases:
    1, cardiovascular diseases, such as: viral myocarditis, chronic heart failure.
    2, hepatitis, such as: viral hepatitis, subacute liver necrosis, chronic active hepatitis.
    3, comprehensive treatment of cancer: can alleviate some adverse reactions caused by radiotherapy, chemotherapy and so on.

    [Usage and Dosage] 1 tablet (granule) at a time, 3 times a day, taken after meals.

    [Storage] sealed, moisture-proof.

    [Tips] Some of the information on this site comes from the Internet and is only used internally by pharmacists or medical staff. It is not a substitute for doctors to diagnose face to face. Please consult a professional pharmacist for specific medications. Please refer to the actual product manual or the actual product for the product content.